摘要
自20世纪20年代以来,"下颌短小后缩畸形、舌后垂和呼吸道阻塞"被确定为Pierre Robin序列征(Pierre Robin syndrome,PRS)。PRS可单独发生或合并其他综合征,如第一、二腮弓综合征及其他相关综合征。PRS可导致新生儿呼吸困难和进食困难,患有严重PRS的儿童可能在出生后不久死于呼吸道阻塞;胎儿期早期诊断可于分娩后得到及时治疗,因此PRS的早期诊断非常重要,可为PRS的早期诊断提供更客观的依据。本文主要介绍近年来影像学早期诊断和三维数字化技术在PRS诊断方面的研究进展。
Since 1920s,a triple combination of micrognathus,drooping tongue and upper airway obstruction has been recognized as Pierre Robin Syndrome(PRS).It occurs alone or in combination with other syndromes,such as first/second branchial arch syndrome and other related syndromes.PRS sequence is clinically associated with dyspnea and feeding difficulties in neonates.Severe PRS cases may die from respiratory obstruction at birth.Thus an early diagnosis is vital during fetal period so that timely treatment may be offered after birth.Therefore more objective diagnostic rationales are required for diagnosing PRS.This review focused upon recent applications of computed tomography(CT)reconstruction and three-dimensional digital technology for an early diagnosis of PRS sequence sign.
作者
陈鑫
崔杰
Chen Xin;Cui Jie(Department of Burns&Plastic Surgery,Affiliated Children’s Hospital,Nanjing Medical University,Nanjing 210008,China)
出处
《临床小儿外科杂志》
CAS
CSCD
2023年第6期597-600,共4页
Journal of Clinical Pediatric Surgery
