摘要
目的了解内淋巴囊肿瘤的临床表现以便进行正确的诊断和治疗。方法总结在我科经手术和病理确诊的6例内淋巴囊肿瘤,分别对其主要症状、临床检查和手术所见以及诊断和鉴别诊断进行分析。结果6例中男性1例,女性5例;年龄分别为28岁、48岁、25岁、38岁、59岁和34岁(平均38.7岁),左耳4例,右耳2例;病程分别为8年、5年、10年、30余年、10年和半年(平均约12.6年)。主要症状:感音神经性耳聋(全聋)4例(伴耳流脓及耳鸣2例,伴耳鸣、面部抽搐和耳流脓、面瘫各1例),1例搏动性耳鸣及面瘫。6例术前均未考虑到内淋巴囊肿瘤,其中拟诊为颈静脉球瘤和胆脂瘤型中耳炎各2例,汗腺腺瘤和颞骨肿瘤各1例。6例中经乳突进路手术2例,经颅-耳-颈或耳-颈联合进路手术4例,术后1例脑脊液漏手术修补愈合。6例经2至8年(平均4.7年)随访均存活。结论内淋巴囊肿瘤非常罕见,无特异性临床表现,容易误诊误治。其病史较长、进展较慢,预后较好。
Objective To understand the clinical characteristics of endolymphatic sac tumor and to optimize its diagnosis and treatment.Methods Six cases diagnosed as endolymphatic sac tumor based on operative findings and pathologcal features were reported and their clinical manifestations,differential diagnosis and surgical approaches were discussed in detail.Results Of the 6 cases,there were one male and five females.Their ages were 28,48,25,38,59 and 34 years separately(mean 38.7 years).The lesions of 4 cases were ...
出处
《中华耳科学杂志》
CSCD
2008年第4期365-369,共5页
Chinese Journal of Otology
关键词
内淋巴囊
肿瘤
Endolymphatic sac
Tumor