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移植治疗肝豆状核变性的临床和研究进展 被引量：4

Research progression of graft in treatment for wilson disease
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摘要 肝豆状核变性(WD)是一种遗传性铜代谢障碍性疾病,表现为铜异常沉积而致多脏器损伤。WD致病基因主要在肝脏表达,提供患者正常的肝细胞(或组织)可以纠正其遗传缺陷,改善铜代谢。此文主要从肝移植和细胞移植角度回顾近年来WD治疗的新进展,为进一步治疗WD提出可能的思路和方法。 Wilson disease is a disease with heritage copper dysbolism. Copper that abnormally deposit on organ made liver, brain damaged. Offering normal hepatic cell （or liver organism） can rectification the genetic defect and improve metabolism of copper. The article reviews the therapy advancement of liver transplantation and cellular transplantation in treating wilson dis ease in order to propose potential treating approach.
作者 阴瑞红 曲云东 林森
机构地区 山东大学第二医院消化内科
出处 《国际消化病杂志》 CAS 2007年第4期275-277,共3页 International Journal of Digestive Diseases
关键词 肝豆状核变性 肝移植 细胞移植 Wilson disease Liver transplantation Cellular transplant
分类号 R742.4 [医药卫生—神经病学与精神病学]
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二级参考文献34

  • 1Xiong Ma,De Kai Qiu,Yan Shen Peng Shanghai Institute of Digestive Diseases, Renji Hospital, Shanghai Second Medical University, Shanghai 200001, China.Immunohistochemical study of hepatic oval cells in human chronic viral hepatitis[J].World Journal of Gastroenterology,2001,7(2):238-242. 被引量：13
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国际消化病杂志
2007年 第4期

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