摘要
目的：探讨肺淋巴管肌瘤病影像表现特点，以提高对肺淋巴管肌瘤病的认识。方法：搜集经病理证实的肺淋巴管肌瘤病6例，均行常规CT和HRCT扫描。结合国内文献病例，对该病的临床及影像学特点进行分析。结果：6例均为女性，年龄35～60岁，平均41岁；就诊时均有不同程度的呼吸困难。且呈进行性加重。在常规扫描上见两肺广泛分布小透亮影及囊状影，分布均匀，囊壁较模糊。HRCT上表现为均匀清楚薄壁小囊腔，囊腔直径几毫米至20mm，壁厚1～2mm，囊气腔被正常肺组织环绕，病变分布无明显上下野、外周或中央差异。结论：肺淋巴管肌瘤病是一种罕见的以细支气管周围血管平滑肌异常增生为特征的疾病，HRCT具有较特征性的表现，是本病主要的影像检查方法。
Objective： To discuss the imaging characteristics of pulmonary lymphangiomyomatosis and make a further understanding of the disease. Methods.. Both conventional CT and HRCT scanning were performed in 6 cases with pulmonary lymphangiomyomatosis proved pathologically. The clinical features and HRCT features were retrospectively analyzed and relevant literature were reviewed. Results： The reported six cases of PLAM were all female, the onset age range between 35-60, average age was 41 years old. The main clinical manifestations of 6 cases was dyspnoea , also assumes carried on the aggravation; 6 cases performed on conventional CT scans , 2 lungs widely distribute the small uniformly thin walls and the follicle shade. The distribution was even. The wall of cysts was fuzzy. HRCT scan showed multiple, well-defined and thin walled cysts in all six cases. The cystic air spaces diameter from a few millimeter to 20 mm. The thickness of the cyst walls was 1～2 mm. There was no peripheral/ central or upper lobe/ lower lobe preponderance of the cysts. Conclusion： Pulmonary lymphangiomyomatosis is a rare lymphangial disease with smooth muscle abnormal hyperplasia. HRCT has diagnostic performance, and it should be used as the first choice for the diagnosis of the disease.
出处
《中国中西医结合影像学杂志》
2007年第6期423-425,共3页
Chinese Imaging Journal of Integrated Traditional and Western Medicine
