摘要
目的探讨少见病因所致肺动脉高压的诊断和治疗。方法回顾性分析2001年2月～2008年3月北京安贞医院诊治的4例少见病因所致肺动脉高压患者的临床、实验室检查、诊断及治疗。结果原发性胆汁性肝硬化、甲状腺功能亢进症、抗磷脂综合征、肺动脉肉瘤等均可引起肺动脉高压，给予相应治疗后病情有不同程度缓解。结论一些少见病因可致肺动脉高压，提高这方面的认识有助于早期诊治，改善患者预后。
Objective To investigate the diagnosis and treatment of pulmonary arterial hypertension （PAH） due to rare causes. Methods The clinical presentation, laboratory testing, diagnosis and treatment of 4 patients with PAH associated with rare causes in Beijing Anzhen Hospital from January 2001 to March 2008 were analysed retrospectively. Results Primary biliary cirrhosis, hyperthyroidism, antiphospholipid syndrome and pulmonary artery sarcoma may cause PAH, which were improved after corresponding diagnosis and management. Conclusion PAH can result from rare causes. The enhancement of its recognition will help earlier diagnosis and treatment and improve the prognosis.
出处
《中国呼吸与危重监护杂志》
CAS
2009年第1期68-71,共4页
Chinese Journal of Respiratory and Critical Care Medicine
关键词
肺动脉高压
病因
原发性胆汁性肝硬化
甲状腺功能亢进症
抗磷脂综合征
肺动脉肉瘤
Pulmonary arterial hypertension
Etiology
Primary biliary cirrhosis
Hyperthyroidism
Antiphospholipid syndrome
Pulmonary artery sarcoma
