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Albright综合征致视神经萎缩1例 被引量:1

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摘要 患者女,13岁.左眼视力下降1周于2007年11月15日住院。患儿出生不久即有皮肤瘙痒,反复起斑疹,2002年曾因骨折行CT检查发现身体多处骨密度不均,12岁月经初潮。查体:头颅及面部无畸形,形体肥胖,体重80kg,乳房增大,双膝以下骨轻度外翻(图1),行动笨拙,手背(图2)、胸背臀下肢(图3)均见色素沉着斑,下肢较密,面积逐渐扩大。眼科检查:视力:右0.6,左0.06,矫正视力:右:-1.75DS→1.0,左:-1.50DS→0.16。左眼屈光间质清晰,瞳孔直径4mm,直接对光反应迟钝,眼底视盘色淡,边界清,视网膜血管走行正常,黄斑区中心凹反光可见。右眼前节及眼底均未见异常。
出处 《中国中医眼科杂志》 2009年第4期239-240,共2页 China Journal of Chinese Ophthalmology
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