摘要
目的:探讨Waardenburg综合征(WS)患者人工耳蜗植入方法及手术前后听力评估和术后言语康复效果。方法:回顾性分析2000-2008年确诊的12例WSⅡ型行人工耳蜗植入患儿的临床资料,所有患儿均经乳突面隐窝进路行人工耳蜗植入,将患儿植入后听力情况与12例内耳发育正常的人工耳蜗植入者(对照组)进行比较。结果:12例WS患儿术中电极植入鼓阶顺利,术后无面瘫及脑脊液漏现象发生,术后听阈与对照组无明显区别。经过超过0.5年的言语康复训练,患儿的听力及言语能力均有不同程度提高。结论:人工耳蜗适用于WS患儿,术前应进行全面的听力学及影像学评估。
Objective：To describe the multi-channel cochlear implantation in patients with Waardenburg syndrome including surgeries,pre and postoperative hearing assessments as well as outcomes of speech recognition.Method：Multi-channel cochlear implantation surgeries have been performed in 12 cases with Waardenburg syndrome typeⅡin our department from 2000 to 2008.All the patients received multi-channel cochlear implantation through transmastoid facial recess approach.The postoperative outcomes of 12 cases were compared with 12 cases with no inner ear malformation as a control group.Result：The electrodes were totally inserted into the cochlears successfully,there was no facial paralysis and cerebrospinal fluid leakage occurred after operation.The hearing threshold in this series were similar to that of the normal cochlear implantation.After more than half a year of speech rehabilitation,the abilities of speech discrimination and spoken language of all the patients were improved compared with that of preoperation.Conclusion：Multi-channel cochlear implantation could be performed in the cases with Waardenburg syndrome,preoperative hearing and images assessments should be done.
出处
《临床耳鼻咽喉头颈外科杂志》
CAS
CSCD
北大核心
2010年第10期436-438,共3页
Journal of Clinical Otorhinolaryngology Head And Neck Surgery
