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自身免疫多腺体综合征的诊断和治疗研究进展 被引量：4

Diagnosis and treatment of polyglandular autoimmune syndrome
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摘要 自身免疫多腺体综合征系指同一个体有2个或2个以上内分泌腺体在自身免疫性炎症侵袭下先后或同时发生功能减退，亦可累及其他非内分泌系统。根据疾病的起病年龄、临床特征及遗传特性，将自身免疫多腺体综合征分为4型。由于症状呈序贯性发生，临床各型的拟诊多在儿科完成。治疗原则是综合分析、替代治疗和主次兼顾。 Polyglandular autoimmune syndromes （PAS） comprises a wide spectrum of autoimmune disorders for autoimmune inflammatory to invade. According to age of presentation, characteristic patterns of disease combinations, and different modes of inheritance, PAS are classified into four subtypes. Actual diagnosis of PAS involves clinical syndromes, serological measurement of organ-specific autoantibodies and subsequent functional testing. Principles of treatment included comprehensive assessment, hormone replacement, general consideration.
作者 晋兴楠（综述） 黄乐（审校）
机构地区 天津市儿童医院内分泌科
出处 《国际儿科学杂志》 2011年第6期554-556,共3页 International Journal of Pediatrics
关键词 多内分泌腺 自身免疫 诊断 治疗 Polyglandular Autoimmune Diagnosis Treatment
分类号 R593.2 [医药卫生—内科学]
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参考文献28

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二级参考文献49

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共引文献29

同被引文献22

引证文献4

二级引证文献6

国际儿科学杂志
2011年 第6期

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