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POEMS综合征临床分析 被引量:2

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摘要 目的总结POEMS综合征的临床特征、治疗方法及预后。方法回顾性分析3例POEMS综合征患者临床资料。结果 3例临床均有不同程度周围神经病、异常球蛋白血症、骨骼损害、脏器肿大、内分泌异常及皮肤改变;1例放弃治疗,1例单用糖皮质激素治疗者停药复发后再次给予糖皮质激素治疗,21个月后死亡;1例应用糖皮质激素联合环磷酰胺治疗者随访至2012年1月仍存活,病情平稳,继续用药控制。结论 POEMS综合征目前无特效治疗方法,环磷酰胺联合糖皮质激素治疗有一定效果。
出处 《中华实用诊断与治疗杂志》 2012年第6期621-622,共2页 Journal of Chinese Practical Diagnosis and Therapy
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参考文献6

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二级参考文献16

  • 1朱卫国,王玉,曾学军,王强,沈悌.POEMS综合征32例临床分析[J].中华内科杂志,2006,45(2):108-111. 被引量:46
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