摘要
目的探讨肾上腺区域Castleman病的临床表现和外科治疗。方法回顾性分析2003--2013年4例。肾上腺区域Castleman病的临床表现、治疗过程及预后，其中男性1例，女性3例，肿瘤直径4～7cm，均以肾上腺肿瘤收入院且缺乏肾上腺肿瘤的特异性临床表现。结果4例肾上腺肿瘤均行手术切除，肿瘤位于肾脏血管和下腔静脉或腹主动脉之间，和周围组织广泛粘连。术后病理报告为Castleman病，其中透明血管型3例（HV）；浆细胞型1例（PC）。4例均认可为良眭疾病，术后失访1例，余3例患者现均存活，无肿瘤复发。结论Castleman病临床上较为少见，而肾上腺区的Castleman病则更为罕见。因此，对于肾上腺区域的肿瘤而又缺乏。肾上腺肿瘤特异性临床表现的患者应考虑到患Castleman病可能，手术切除肿瘤疗效可靠，但确诊需依靠术后的病理检查。
Objective To explore the clinical manifestations and surgical treatment of Castleman disease of adrenal region. Methods The clinical performance, treatment and prognosis of 4 cases of Castleman disease of the adrenal region which include 1 male and 3 females from 2003 to 2013 were reviewed retrospectively. They were admitted to the hospital due to adrenal region tumors but without the specific clinical manifestations of adrenal tumor. The diameters of tumors were 4 -7 cm. Results All 4 cases underwent surgical resection, the tumors were located between the kidney blood vessels and the inferior vena cava or abdominal aorta, and kept extensive adhesions with surrounding tissues, and were confirmed as Castleman disease by postoperative pathology experiment, which included three cases of hyaline vascular type （HV） and 1 case of plasma cell type（PC）. 4 patients were recognized as benign disease, one of them was lost to follow and the other 3 patients were alive without evidence of recurrence. Conclusion Castleman disease is rarely and even more rare in the adrenal region disease. Therefore, the patient with adrenal region tumors and lack of adrenal tumor-specific clinical manifestations should be considered as Castleman disease. Surgical resection of the tumor is effective and reliable, but the diagnosis must rely on the postoperative pathological examination.
出处
《中华全科医学》
2014年第3期399-400,共2页
Chinese Journal of General Practice
