期刊文献+

平山病的过屈位MRI表现及其临床价值

Features and Diagnostic Value of Flexion Position MRI in the Hirayama Disease
原文传递
导出
摘要 目的:探讨平山病的过屈位颈椎MRI特征性影像学表现及其临床诊断价值。方法:总结分析经临床证实的5例平山病患者的临床及MRI资料,并结合相关文献报道进行回顾性分析。所有患者均行常规生化检查,脑脊液检查,肌电图检查及肌肉活检。结果:5例均为青少年男性,呈单侧上肢远端无力伴萎缩,其中1例患者累及另一侧,尺侧肌萎缩明显,上肢呈斜坡样改变,均无感觉障碍和锥体束征;肌电图检查显示神经源性改变,提示受损节段多在下颈髓前角细胞。屈颈MRI检查均可见下颈髓前移、硬脊膜外间隙增宽,可见迂曲条状血管流空影。结论:平山病的过屈位MRI表现具有一定的特征性,对平山病的诊断具有重要价值。 Objective:To investigate the clinical manifestation and diagnostic value of flexion position MRI in the Hirayama Disease.Methods:Retrospective analysis of 5 clinically proven Hirayama patients MRI data and combined with other reports.The routine biochemical examination,cerebrospinal fluid examination,electromyogram and muscle biopsy were performed for all the cases.Results:Hirayama disease predominantly in young males in puberty,with muscle weakness and atrophy on one upper limb,and one case with the other side,the brachioradialis was spared(oblique amyotrophy),but without sensory disorder or pyramidal sign.EMG indicated that the impairment of spinal anterior cells were limited to the arm relevant segments and both sides were involved.During neck flexion,the spinal cord was displaced forward and flattened,in which there were distorting or stripe flow void signals with enhancement.Conclusion:Flexion position MRI of Hirayama Disease had characteristic appearances that had significant values for the diagnosis of Hirayama disease.
出处 《现代生物医学进展》 CAS 2014年第12期2339-2342,共4页 Progress in Modern Biomedicine
关键词 平山病 MRI 屈颈位 诊断 Hirayama disease Magnetic resonance imaging Flexion position Diagnosis
  • 相关文献

参考文献21

  • 1Hirayamak K, Tsubakl T, Toyokura Y, et al. Juvenile Muscular Atrophy of Unilateral Upper Extremity [J]. Neurology, 1963, 13 (3): 373-380.
  • 2Tashiro K, Kikuchi S, Itoyama Y, et al. Nationwide survey of juvenile muscular atrophy of distal upper extremity (Hirayama disease) in Japan[J]. Amyotroph Lateral Scler Other Motor Neuron Disord, 2006, 7(1): 38-45.
  • 3周波,周东.平山病国内文献报道192例分析[J].华西医学,2009,24(2):409-412. 被引量:14
  • 4徐迎胜,郑菊阳,张朔,张俊,康德宣,樊东升.平山病的神经电生理学研究[J].中国现代神经疾病杂志,2008,8(4):314-317. 被引量:13
  • 5李志军,胡晓晴,唐娜.平山病的临床神经电生理学特点[J].神经损伤与功能重建,2008,3(4):242-245. 被引量:8
  • 6Chela CJ, Chen CM, Wu C1, et al. Hirayama Disease: MR Diagnosis [J]. AJNR, 1998, 19(2): 365-368.
  • 7Mukai E, Mat suo T, Muto, et al. Magnetic Resonance Imaging of Ju- veniletype Distal and Segmental Muscular Atrophy of the Upper Ex- tremities[J]. Rinsho Shinkeigaku, 1987, 27(1): 99-107.
  • 8Hirayama K. Juvenile muscular atrophy of unilateral upper extremity (hirayama disease)-half-century progress and establishment since its discovery[J]. Brain Nerve, 2008, 60:17-29.
  • 9Hiayama K, Tokumaru Y. Cervical dural sac and spinal cord in juvenile muscular atrophy of distal upper extremity [J]. Neurology, 2000, 54(10): 1922-1926.
  • 10Baba Y, Nakajima M, Utsunomiya H. Magnetic resonance imaging of thoracic epidural venous dilation in Hirayama disease [J]. Neurology,2004, 62(8): 1426-1428.

二级参考文献113

共引文献59

相关作者

内容加载中请稍等...

相关机构

内容加载中请稍等...

相关主题

内容加载中请稍等...

浏览历史

内容加载中请稍等...
;
使用帮助 返回顶部