摘要
【目的】分析复杂性先天性心脏病 (复杂先心病 )变类型与心脏位置之间的相关性。【方法】收集 1986年 9月至2 0 0 0年 2月期间 81例复杂先心病资料 ,就病变类型与心脏位置相关性作一分析。【结果】在正常或镜面右位心中 ,复杂先心病发病率与性别无关 ,但在心脏位置异常情况下男女之间有显著差别 ( 4∶1) ,本组就诊年龄平均在 4岁 ,肺动脉瓣闭锁及左心室发育不全综合症常构成新生儿急诊。主要病变为 :大动脉错位 38%、单心室 16 %、动脉共干 13%、三尖瓣闭锁 10 %。正常或镜面右位心中大动脉转位 71%系完全型 ,而心脏异位中 6 9%系矫正型 ,此类畸形常伴畸形为室间隔缺损及肺动脉瓣狭窄。左旋心、孤立左位心常伴有最复杂心内畸形、畸型数达 2～ 8(平均 4 89± 1 76 )。本组病例中镜面右位心伴复杂心内畸形并非少见。还发现 2例完全型体静脉异位引流。【结论】复杂先心病病变类型与心脏位置有一定联系。左旋心、孤立左位心常系最复杂心内畸形。
Objective To study the pathologic change of complex CHD and the relationship between complex CHD with the positional anomalies of the heart. Method From Sep., 1986 to 2000 Feb., 81 cases of complex CHD in our hospital were accumulated. The pathologic change correlated with the various positional anomalies was analysed. Results In the incidence of complex CHD, there were no sex different distributions in normal or mirror image dextrocardia, but with significant differences in positional anomalies of the heart, male: female was 4∶1. The average age came to clinic was 4 years old, PA and HLHS usually as a emergency in neonate. The incidence of major pathologic change in complex CHD was: TGA 38%, SV 16%, common trunk 13%, TA 10%. 71% of complete TGA in normal or mirror image dextrocardia and 69% of correlated TGA happened in positional anomalies of the heart. The combined lesions in TGA was VSD and PS. Levoversion and isolated levocardia always accompanied with the most complex lesions, the number of defects from 2 to 8 (4 89±1 76, average). In our group, complex CHD was not uncommon in mirror dextrocardia. Two scarcely cases of TASVD found in this group. Conclusions The pathologic anatomy of complex CHD may have close relationship with the positional anomalies of the heart. Levoversion and isolated levocardia were the most complex anomalies of the heart.
出处
《中山医科大学学报》
CSCD
北大核心
2001年第2期125-128,132,共5页
Academic Journal of Sun Yat-sen University of Medical Sciences
基金
广东省科委"五个一"工程基金项目
