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血栓性血小板减少性紫癜发病机制及诊疗进展 被引量:3

Update on the diagnosis and treatment of thrombotic thrombocytopenic purpura
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摘要 血栓性血小板减少性紫瘢(thrombotic throm—bocytopenic purpura,TTP)临床较少见,发病率约为3.7/100万,发病年龄多为10~40岁,女性较多见,男女比例约1:2。该病起病急骤,未及时治疗致死率可达90%。 Thrombotic thrombocytopenic purpura(TTP)is a disease characterized by thrombocytopenia and microvascular thrombosis.The disease is acute,the condition is dangerous,and the early death rate can reach 90%.This article intends to review the pathogenesis,diagnosis and treatment progress of TTP in order to improve the understanding and treatment of TTP among clinicians and improve the prognosis of patients with TTP.
出处 《临床血液学杂志》 CAS 2018年第6期891-894,共4页 Journal of Clinical Hematology
基金 山西省科技创新团队(No:201605D131044-05) 山西医科大学大学生创新创业校级项目(No:20160256)
关键词 血栓性血小板减少性紫瘢 发病机制 诊断 治疗 thrombotic thrombocytopenic purpura pathogenesis diagnosis treatment
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