摘要
目的分析平山病病人颈髓MRI表现特征,探讨其诊断价值。方法回顾分析临床确诊的5例平山病病人颈髓MRI资料。5例病人均起病隐匿,病变局限于上肢前臂肌肉,均为单侧上肢前臂受累,对5例病人均行颈椎自然位和过屈位T1WI、T2WI序列矢状位及C3~C7横轴位T2WI序列平扫,过屈位及自然位T1WI矢状位和横轴位FSET1WI增强扫描;所有病人均行常规生化检查和脑脊液检查、肌电图检查和肌肉活检。结果 5例病人均有颈椎生理曲度变直,自然体位均见低位脊髓萎缩变扁,脊髓内T2WI序列可见高信号;屈颈位均可见颈髓前移、变平,硬脊膜前移,硬膜外隙增宽,硬膜外隙可见血管流空信号,增强见强化的静脉丛。结论平山病病人颈髓MRI屈颈位存在特殊的颈髓前移、变平,硬脊膜前移,对平山病的诊断及鉴别诊断具有重要价值。
Objective To analyze the MRI feature of Hirayama disease and assess its diagnostic value. Methods MRI data of five patients with clinically-confirmed Hirayama disease were retrospectively reviewed.The onset of the disease was insidious in all the five patients,the lesion was noted to be confined to the forearm muscles,and unilateral forearm only was involved.Cervical neutral and flexion T1 WI,T2WI sequence sagittal and transverse T2 WI C3-C7 sequence scanning were done,enhancement scanning of over-flexion and neutral T1 WI sagittal and axial FSET1 WI were performed.Routine biochemical examination,cerebrospinal fluid examination,electromyography check and muscle biopsy were carried out. Results Cervical physiological curvature straightened,low-set myelatrophy could be seen on neutral posture,abnormal high signal could be seen in T2 WI sequences in spinal cord.On flexion,the following features could be seen：anterior displacement of cervical cord,cord flattening,anterior displacement of dura,broadening of epidural space,empty blood flow signals in epidural space,and intensive venous plexus. Conclusion Special anterior displacement of cervical cord,cord flattening,and anterior displacement of dura on flexion position are MRI findings in patients with Hirayama disease,these features are important in the diagnosis and differential diagnosis of the disease.
出处
《齐鲁医学杂志》
2016年第1期64-66,共3页
Medical Journal of Qilu
关键词
青少年上肢远端肌萎缩症
磁共振成像
诊断
teenagers upper limbs distal muscular atrophy
magnetic resonance imaging
diagnosis
