摘要
先天性膈疝（CDH）是指由单侧或双侧膈肌发育缺损，腹腔脏器疝人胸腔为主要病理生理改变的一种先天性疾病。该病发病率约1／2000-1／5000。随着呼吸支持技术的发展以及膈疝患儿生后标准化治疗方案的初步形成，CDH患儿离院前的存活率明显提高。但目前CDH患儿的总体存活率差异仍然很大，尤其是不同类型及不同病情程度的膈疝患儿的存活率有显著性差异。患儿术后仍面临着肺发育不全导致的种种威胁。本文对膈疝患儿的肺功能检测进行综述。
Congenital diaphragmatic hernia （CDH） occurs one in 2000 - 5000 births annually. Malformation of diaphragm allows abdominal organs to thrust into chest cavity, hindering proper lung formation. The survival rate of CDH children has increased thanks to on the development of technical respiratory supports and after - birth interventions. However, it is obvious that there is a big gap between survival rate of CDH and different types and severity. Patients still faces various threats caused by pulmonary hypoplasia. Lung function test of congenital diaphragmatic hernia were also reviewed.
出处
《中华小儿外科杂志》
CSCD
2016年第6期476-480,共5页
Chinese Journal of Pediatric Surgery
关键词
疝
横膈
高血压
肺性
支气管肺发育不良
Hernia, Diaphragmatic
Hypertension, pulmonary
Bronchopulmonary dysplasia
