摘要
目的对3例以全血细胞减少为茸发症状的成人继发性噬血细胞综合征（rIPS）患者的临床表现和骨髓象、骨髓病理进行分析，以期提高对该病的诊治水平。方法回顾性分析3例患者的临床表现、化验和骨髓检查资料。结果以全血细胞减少为首发症状的成人继发性噬血细胞综合征1例治愈．1例好转，1例死亡。结论成人继发性噬血细胞综合征病情较凶险，以全血细胞减少为首发症状的成人继发性噬血细胞综合征临床易误诊，从而延误治疗，早期糖皮质激素及免疫球蛋白的应用能减轻炎症反应，控制病情发展。
Objective Improving diagnosis and treatment,we have reported three adult patients with secondary bemophagocytic syndrome, characterized by pancytopenia. Methods We retrospectively have analyzed the clinical feature, the laboratory examination, and the histomorphometry,＇patholo~ of bone morrow in three adult patients. Results In the three patients with HPS, one case was cure, one case improved and the other death. Conclusion Secondary. HPS in adult is a rare but life-threatening disease, and early therapy with eorticosteroids maybe suppress the hypereytokinemia, reduce systemic inflammatory, and improve HPS prognosis.
出处
《世界中医药》
CAS
2016年第B06期2225-2226,共2页
World Chinese Medicine
