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左心室受累的致心律失常心肌病研究进展 被引量：3

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摘要 目前在临床上发现致心律失常右心室心肌病中有许多合并累及左心室的病例,还有部分单纯累及左心室的致心律失常心肌病。左心室受累的致心律失常性心肌病流行病学研究不多,临床特征主要表现为左心室起源的室性心律失常,早期可能只有心电学的改变,左心室结构无明显异常,磁共振检查可见左心室延迟增强等影像学异常,临床预后比单纯累及右心室更差,心原性猝死发生率高。左心室受累的致心律失常心肌病的致病突变基因同样以编码桥粒蛋白的基因突变为主,但其不同于右心室心肌病(常见突变基因PKP2),DSP基因是其最常见的突变基因。
作者 范思洋 樊晓寒
机构地区 中国医学科学院北京协和医学院国家心血管病中心阜外医院心律失常中心
出处 《中国循环杂志》 CSCD 北大核心 2016年第9期931-934,共4页 Chinese Circulation Journal
关键词 综述 心肌疾病 心律失常 心性
分类号 R541 [医药卫生—心血管疾病]
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参考文献28

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二级参考文献22

  • 1黄洁,郑哲,胡盛寿,杨跃进,赵世华,赵红,宋来凤,宋云虎,蒋世良.致心律失常性右心室心肌病累及左心室的临床病理分析[J].中国循环杂志,2007,22(4):278-281. 被引量：10
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共引文献17

同被引文献21

引证文献3

二级引证文献5

中国循环杂志
2016年 第9期

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