摘要
阵发性睡眠性血红蛋白尿症(PNH)是一种克隆性造血干细胞功能紊乱所致罕见性骨髓功能衰竭性疾病,以血管内溶血性贫血,全血细胞减少和血栓为表现。PNH虽是良性疾病,但其并发症严重影响患者生活质量和生存时间,其中最常见严重并发症是血栓。
Paroxysmal nocturnal haemoglobinuria（ PNH） is a clonal hematopoietic stem cell disease characterized by intravascular hemolytic anemia,pancytopenia and thrombosis. Although PNH is an non-malignant disease,its complications have very negative impacts on patient＇s quality of life. The most common serious complication is thrombosis formation.
出处
《基础医学与临床》
CSCD
2017年第1期128-132,共5页
Basic and Clinical Medicine
关键词
阵发性睡眠性血红蛋白尿
血栓
paroxysmal nocturnal haemoglobinuria
thrombosis
