摘要
18岁女性患者,以腹痛、发热起病,进而出现肝酶升高及全血细胞减少、癫痫发作等,腹部CT提示假性肠梗阻,骨髓细胞学检查有噬血细胞,血清学检查抗核抗体阳性,EB病毒感染再激活。最终确诊为系统性红斑狼疮、EB病毒感染,并发假性肠梗阻和噬血细胞综合征。
An 18-year old female patient,began with abdominal pain,and fever,then developed pancytopenia,transaminase elevation and seizure.Computed tomography(CT)revealed intestinal pseudo-obstruction(IPO)and bone marrow aspirate proved hemophagocytes.Serologic tests for Epstein-Barr virus(EBV)indicated its reactivation and antinuclear antibodies positive.This case demonstrates that hemophagocytic syndrome(HPS)and concomitant IPO associated with EBV reactivation can occur as clinical manifestations of systemic lupus erythematosus(SLE)flare.
作者
许书添
董建华
李世军
XU Shutian;DONG Jianhua;LI Shijun(National Clinical Research Center of Kidney Diseases,Jinling Hospital,Nanjing University School of Medicine,Nanjing 210016,China)
出处
《肾脏病与透析肾移植杂志》
CAS
CSCD
北大核心
2019年第3期293-297,共5页
Chinese Journal of Nephrology,Dialysis & Transplantation
关键词
系统性红斑狼疮
噬血细胞综合征
巨噬细胞活化综合征
假性肠梗阻
systemic lupus erythematosus
hemophagocytic syndrome
macrophage activation syndrome
intestinal pseudo-obstruction
