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血小板无力症致卵巢血肿误诊为卵巢畸胎瘤一例

Hemorrhagic ovarian cysts misdiagnosed as ovarian teratoma due to Glanzmann thrombasthenia:a case report
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摘要 血小板无力症是一种罕见的常染色体隐性遗传性疾病,女性多表现为月经过多,少数青春期患者则表现为卵巢血肿,容易误诊为卵巢囊肿而导致手术。反复出血加剧原发疾病严重程度,从而导致围手术期难以控制的腹腔内出血。因此,对于合并血小板无力症的青春期女性因卵巢囊肿就诊,接诊医师应仔细辨认影像学结果,尽量避免手术,减少误诊误治。 Glanzmann thrombasthenia is a rare autosomal recessive disorder,characterized by excessive men-struation in women and ovarian hematoma in a few adolescent patients,which is easily misdiagnosed as an ovarian cyst and leads to surgery.Recurrent bleeding can exacerbate the severity of the primary disease,which can easily lead to un-controllable intra abdominal bleeding during the perioperative period.Therefore,for the treatment of adolescent female ovarian cyst patients with glanzmann thrombasthenia,the attending physician should carefully identify the imaging re-sults,try to avoid surgery and reduce misdiagnosis and misdiagnosis.
作者 史元湘 曹莉莉 吴治敏 杜凌 SHI Yuan-xiang;CAO Li-li;WU Zhi-min;DU Ling(Department of Obstetrics and Gynecology,First Affiliated Hospital,Army Military Medical University,Chongqing 400038,CHINA;Department of Female Tumor,Guiyang Maternity and Child Health Care Hospital,Guiyang 550001,Guizhou,CHINA)
出处 《海南医学》 CAS 2023年第11期1633-1634,共2页 Hainan Medical Journal
关键词 卵巢囊肿 血小板无力症 出血性疾病 青春期 血小板输注 Ovarian cyst Glanzmann thrombasthenia Hemorrhagic diseases Adolescent Platelet transfusion
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