弥漫大B细胞淋巴瘤（Diffuse large B cell lymphoma,DLBCL）是一种好发于血液系统的恶性肿瘤,原发肾脏DLBCL较为罕见,占结外淋巴瘤比例不足0.7%^（[1]）。因原发性肾脏DLBCL恶性程度高、预后差,临床医师对其缺乏认识。我们回顾性分析...弥漫大B细胞淋巴瘤（Diffuse large B cell lymphoma,DLBCL）是一种好发于血液系统的恶性肿瘤,原发肾脏DLBCL较为罕见,占结外淋巴瘤比例不足0.7%^（[1]）。因原发性肾脏DLBCL恶性程度高、预后差,临床医师对其缺乏认识。我们回顾性分析了我院收治的9例原发性肾脏DLBCL患者的临床资料,归纳总结其临床特点。展开更多
Objective To investigate the clinical characteristics of primary adult renal sarcoma.Methods A total of 1654 cases with adult renal tumors were treated during 1985 to 2009 in Peking Union Medical College Hospital.Of a...Objective To investigate the clinical characteristics of primary adult renal sarcoma.Methods A total of 1654 cases with adult renal tumors were treated during 1985 to 2009 in Peking Union Medical College Hospital.Of all,17 cases were diagnosed as primary renal sarcoma and underwent radical nephrectomy.The clinical features of 17 such patients were retrospectively analyzed.Results The first symptom of 10(59%) cases in all renal sarcomas was abdominal mass.The pathological diagnosis was leiomyosarcoma(7 cases),rhabdomyosarcoma(2 cases),malignant fibrous histiocytoma(2 cases),low-differentiated sarcoma(2 cases),chromophobe renal cell carcinoma coexisting with liposarcoma(1 case),fibrosarcoma(1 case),embryonic sarcoma(1 case) and leiomyosarcoma(1 case).One patient died of tumor thrombus of the inferior vena cava during surgery.Finally,15 cases were regularly followed up for 4 to 60 months.Till now,1 had tumor-free survival for 9 months,and the other 14 cases died 2-38 months after the operation with a median survival time of 18(range,5-60) months.The median survival time of leiomyosarcoma group was 28(range,11-60) months,and 2 cases of malignant fibrous histiocytoma died 4 and 8 months after the operation respectively.Conclusions The primary renal sarcoma has the clinical symptom similar with advanced renal cell carcinoma and has poor prognosis.Leiomyosarcoma might have relative good prognosis.展开更多
IntroductionAngiosarcomas are rare highly malignant neoplasm that make up less than 2% of all soft-tissue sarcomas. Only 40 renal cases have been described. Their origin is from endothelial cells. They are frequently ...IntroductionAngiosarcomas are rare highly malignant neoplasm that make up less than 2% of all soft-tissue sarcomas. Only 40 renal cases have been described. Their origin is from endothelial cells. They are frequently hemorrhagic tumors, being able to simulate a retroperitoneal hematoma or cause massive hematuria. We present a case of primary renal angiosarcoma and emphasize its hemorrhagic behavior.展开更多
文摘弥漫大B细胞淋巴瘤（Diffuse large B cell lymphoma,DLBCL）是一种好发于血液系统的恶性肿瘤,原发肾脏DLBCL较为罕见,占结外淋巴瘤比例不足0.7%^（[1]）。因原发性肾脏DLBCL恶性程度高、预后差,临床医师对其缺乏认识。我们回顾性分析了我院收治的9例原发性肾脏DLBCL患者的临床资料,归纳总结其临床特点。
文摘Objective To investigate the clinical characteristics of primary adult renal sarcoma.Methods A total of 1654 cases with adult renal tumors were treated during 1985 to 2009 in Peking Union Medical College Hospital.Of all,17 cases were diagnosed as primary renal sarcoma and underwent radical nephrectomy.The clinical features of 17 such patients were retrospectively analyzed.Results The first symptom of 10(59%) cases in all renal sarcomas was abdominal mass.The pathological diagnosis was leiomyosarcoma(7 cases),rhabdomyosarcoma(2 cases),malignant fibrous histiocytoma(2 cases),low-differentiated sarcoma(2 cases),chromophobe renal cell carcinoma coexisting with liposarcoma(1 case),fibrosarcoma(1 case),embryonic sarcoma(1 case) and leiomyosarcoma(1 case).One patient died of tumor thrombus of the inferior vena cava during surgery.Finally,15 cases were regularly followed up for 4 to 60 months.Till now,1 had tumor-free survival for 9 months,and the other 14 cases died 2-38 months after the operation with a median survival time of 18(range,5-60) months.The median survival time of leiomyosarcoma group was 28(range,11-60) months,and 2 cases of malignant fibrous histiocytoma died 4 and 8 months after the operation respectively.Conclusions The primary renal sarcoma has the clinical symptom similar with advanced renal cell carcinoma and has poor prognosis.Leiomyosarcoma might have relative good prognosis.
基金a grant from the Outstanding Youth Foundation of Jilin Pro-vincial Scientific Development Program (No.20060103)
文摘IntroductionAngiosarcomas are rare highly malignant neoplasm that make up less than 2% of all soft-tissue sarcomas. Only 40 renal cases have been described. Their origin is from endothelial cells. They are frequently hemorrhagic tumors, being able to simulate a retroperitoneal hematoma or cause massive hematuria. We present a case of primary renal angiosarcoma and emphasize its hemorrhagic behavior.
