皮下脂膜炎样T细胞淋巴瘤（subcutaneous panniculitislike T cell lymphoma，SPTCL）是一种少见的主要累及皮下脂肪组织且与脂膜炎相似的原发性皮肤淋巴瘤。其发病率低，预后差，目前治疗以联合化疗为主。现将我科使用硼替佐米联合化...皮下脂膜炎样T细胞淋巴瘤（subcutaneous panniculitislike T cell lymphoma，SPTCL）是一种少见的主要累及皮下脂肪组织且与脂膜炎相似的原发性皮肤淋巴瘤。其发病率低，预后差，目前治疗以联合化疗为主。现将我科使用硼替佐米联合化疗治疗2例SPTCL患者报道如下。展开更多
Introduction Subcutaneous panniculitis-like T-cell lymphoma (SPTCL) is a rare cytotoxic T-cell lymphoma that accounts for less than 1% of all peripheral T-cell lymphomas.SPTCL is characterized by multiple subcutaneous...Introduction Subcutaneous panniculitis-like T-cell lymphoma (SPTCL) is a rare cytotoxic T-cell lymphoma that accounts for less than 1% of all peripheral T-cell lymphomas.SPTCL is characterized by multiple subcutaneous nodules or plaques that occur in the extremities,and it has a poor prognosis if accompanied by hemophagocytic syndrome.The histopathological findings and immunophenotype of SPTCL are specific and can help to confirm the diagnosis.We herein report such a rare case involving a woman with a single facial lesion.展开更多
文摘皮下脂膜炎样T细胞淋巴瘤（subcutaneous panniculitislike T cell lymphoma，SPTCL）是一种少见的主要累及皮下脂肪组织且与脂膜炎相似的原发性皮肤淋巴瘤。其发病率低，预后差，目前治疗以联合化疗为主。现将我科使用硼替佐米联合化疗治疗2例SPTCL患者报道如下。
基金supported by the CAMS Innovation Fund for Medical Sciences(No.CIFMS-2017-I2M-1-107)
文摘Introduction Subcutaneous panniculitis-like T-cell lymphoma (SPTCL) is a rare cytotoxic T-cell lymphoma that accounts for less than 1% of all peripheral T-cell lymphomas.SPTCL is characterized by multiple subcutaneous nodules or plaques that occur in the extremities,and it has a poor prognosis if accompanied by hemophagocytic syndrome.The histopathological findings and immunophenotype of SPTCL are specific and can help to confirm the diagnosis.We herein report such a rare case involving a woman with a single facial lesion.
